Search results

  1. 1.
    0565785 - ÚŽFG 2023 eng A - Abstract
    Vochozková, Petra - Auch, H. - Nemesh, Kateryna - Nguyen, The Duong - Sekáč, David - Kamenná, Eva - Baxa, Monika - Klíma, Jiří - Ardan, Taras - Juhás, Štefan - Levinská, Božena - Juhásová, Jana - Keller, J. - Klempíř, J. - Motlík, Jan - Klymiuk, N. - Ellederová, Zdeňka
    MINIPIG MODELS OF HUNTINGTON'S DISEASE AT PIGMOD CENTER.
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 93, Suppl 1 (2022), A16-A16. ISSN 0022-3050. E-ISSN 1468-330X.
    [EHDN Plenary Meeting. 16.09.2022-18.09.2022]
    Institutional support: RVO:67985904
    Keywords : minipig * Pigmod Centre
    OECD category: Neurosciences (including psychophysiology
    Permanent Link: https://hdl.handle.net/11104/0337643
     
     
  2. 2.
    0551153 - ÚŽFG 2022 CZ cze A - Abstract
    Motlík, Jan
    Vytváření transgenních modelů závažných, dosud neléčitelných lidských onemocnění u miniprasat.
    Biologické dny 2021. Brno: ČSBS, 2021. s. 1-2.
    [Biologické dny 2021. 06.09.2021-07.09.2021, Brno]
    Institutional support: RVO:67985904
    Keywords : minipig
    OECD category: Genetics and heredity (medical genetics to be 3)
    Permanent Link: http://hdl.handle.net/11104/0326600
     
     
  3. 3.
    0537089 - ÚŽFG 2021 DK eng A - Abstract
    Ardan, Taras - Zemanová, Lucie - Ellederová, Zdeňka - Drutovič, Saskia - Studenovská, Hana - Popelka, Štěpán - Vodičková Kepková, Kateřina - Rohiwal, Sonali Suresh - Sedláčková, Miroslava - Motlík, Jan
    Nanofibrous membranes reveal better properties for culturing of RPE cells in comparison with commercial scaffolds.
    Acta Ophthalmologica. Roč. 97, S263 (2019), s. 263-263. ISSN 1755-375X. E-ISSN 1755-3768.
    [European Association for Vision and Eye Research Conference. 17.10.2019-19.10.2019, Nice]
    Keywords : retinal pigment epithelium
    OECD category: Ophthalmology; Polymer science (UMCH-V)
    https://onlinelibrary.wiley.com/doi/abs/10.1111/j.1755-3768.2019.5166
    Permanent Link: http://hdl.handle.net/11104/0314836
     
     
  4. 4.
    0498987 - ÚŽFG 2019 RIV GB eng A - Abstract
    Vallés, A. - Brouwers, C. - Pintauro, R. - Snapper, J. - Bohuslavová, Božena - Sogorb-Gonzales, M. - Fodale, V. - Bresciani, A. - Ellederová, Zdeňka - Blits, B. - Motlík, Jan - van Deventer, S. - Evers, M. - Konstantinová, P.
    SUSTAINED MUTANT HUNTINGTIN LOWERING IN THE BRAIN AND CEREBROSPINAL FLUID OF HUNTINGTON DISEASE MINIPIGS MEDIATED BY AAV5-MIHTT GENE THERAPY.
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A89-A90. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : minipig * Huntingtin
    OECD category: Genetics and heredity (medical genetics to be 3)
    Permanent Link: http://hdl.handle.net/11104/0291269
     
     
  5. 5.
    0498986 - ÚŽFG 2019 RIV GB eng A - Abstract
    Šmatlíková, Petra - Askeland, G. - Vaškovičová, Michaela - Klíma, Jiří - Motlík, Jan - Eide, L. - Ellederová, Zdeňka
    GRADUAL ACCUMULATION OF OXIDATIVE STRESS AND ITS ASPECTS IN PRIMARY PORCINE FIBROBLASTS EXPRESSING MUTATED HUNTINGTIN.
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A13-A13. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : oxidative stress * Huntingtin
    OECD category: Neurosciences (including psychophysiology
    Permanent Link: http://hdl.handle.net/11104/0291268
     
     
  6. 6.
    0498981 - ÚŽFG 2019 RIV GB eng A - Abstract
    Rodinová, M. - Křížová, J. - Štufková, H. - Bohuslavová, Božena - Askeland, G. - Dosoudilová, Z. - Juhás, Štefan - Ellederová, Zdeňka - Zeman, J. - Eide, L. - Motlík, Jan - Hansíková, H.
    LONGITUDINAL VIEW OF MITOCHONDRIAL BIOENERGETICS IN SKELETAL MUSCLE OF PREMANIFEST TRANSGENIC MINIPIG MODEL FOR HUNTINGTON'S DISEASE.
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A23-A24. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : transgenic minipig model * Huntington´s disease
    OECD category: Neurosciences (including psychophysiology
    Permanent Link: http://hdl.handle.net/11104/0291266
     
     
  7. 7.
    0498979 - ÚŽFG 2019 RIV GB eng A - Abstract
    Rieke, L. - Schubert, R. - Matheis, T. - Muratori, L. M. - Freisfeld, F. - Motlík, Jan - Fels, M. - Kemper, N. - Schuldenzucker, V. - Reilmann, R.
    VOCALISATION AS A VIABLE ASSESSMENT FOR MINIPIGS TRANSGENIC FOR THE HUNTINGTON GENE?
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A23-A23. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : minipig * Huntington gene
    OECD category: Neurosciences (including psychophysiology
    Permanent Link: http://hdl.handle.net/11104/0291265
     
     
  8. 8.
    0498977 - ÚŽFG 2019 RIV GB eng A - Abstract
    Matheis, T. - Schubert, R. - Rieke, L. - Schuldenzucker, V. - Motlík, Jan - Fels, M. - Kemper, N. - Niuratori, L. - Reilmann, R.
    BIOLOGICAL MOTION DETECTION - A COGNITIVE TEST FOR PIGS TRANSGENIC FOR THE HUNTINGTON GENE?
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A22-A22. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609; GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : transgenic pig * Huntingon gene
    OECD category: Neurosciences (including psychophysiology
    Permanent Link: http://hdl.handle.net/11104/0291263
     
     
  9. 9.
    0498974 - ÚŽFG 2019 RIV GB eng A - Abstract
    Klíma, Jiří - Evers, M. - Miniariková, J. - Juhás, Štefan - Vallés, A. - Bohuslavová, Božena - Juhásová, Jana - Kupcová Skalníková, Helena - Vodička, Petr - Valeková, Ivona - Brouwers, C. - Blits, B. - Lubelski, J. - Kovářová, Hana - van Deventer, S. - Petry, H. - Motlík, Jan - Konstantinová, P. - Ellederová, Zdeňka
    AAV5-MIHTT GENE THERAPY DEMONSTRATES BROAD DISTRIBUTION AND STRONG HUMAN MUTANT HUNTINGTIN LOWERING IN A HUNTINGTON DISEASE MINIPIG MODEL.
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A89-A89. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : AAV5-MHTT gene therapy * Huntingtonˇs disease
    OECD category: Genetics and heredity (medical genetics to be 3)
    Permanent Link: http://hdl.handle.net/11104/0291258
     
     
  10. 10.
    0498968 - ÚŽFG 2019 RIV GB eng A - Abstract
    Baxa, Monika - Bohuslavová, Božena - Kučerová, S. - Mačáková, Monika - Klempíř, J. - Motlík, Jan - Ellederová, Zdeňka
    BATTERY OF TESTS ASSESSED TO MONITOR MOTOR AND COGNITIVE FUNCTIONS OF TRANSGENIC HUNTINGTON'S DISEASE MINIPIG MODEL.
    Journal of Neurology Neurosurgery and Psychiatry. Roč. 89, S1 (2018), A22-A22. ISSN 0022-3050. E-ISSN 1468-330X.
    [Plenary Meeting of the European Huntington´s Disease Network (EHDN). 14.09.2018-16.09.2018, Vienna]
    R&D Projects: GA MŠMT(CZ) LO1609
    Institutional support: RVO:67985904
    Keywords : minipig model * Huntington´s disease * cognitive functions
    OECD category: Neurosciences (including psychophysiology
    Permanent Link: http://hdl.handle.net/11104/0291249
     
     

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