Deterioration of mitochondrial bioenergetics and ultrastructure impairment in skeletal muscle of a transgenic minipig model in the early stages of Huntington's disease

RODINOVÁ, M., KŘÍŽOVÁ, J., ŠTUFKOVÁ, H., BOHUSLAVOVÁ, Božena, ASKELAND, G., DOSOUDILOVÁ, Z., JUHÁS, Štefan, JUHÁSOVÁ, Jana, ELLEDEROVÁ, Zdeňka, ZEMAN, J., EIDE, L., MOTLÍK, Jan, HANSÍKOVÁ, H. Deterioration of mitochondrial bioenergetics and ultrastructure impairment in skeletal muscle of a transgenic minipig model in the early stages of Huntington's disease. Disease Models & Mechanisms. 2019, 12(7), dmm038737. ISSN 1754-8403. E-ISSN 1754-8411. Available: doi: 10.1242/dmm.038737.